Intraoral myoepithelial carcinoma is a rare disease. It can be frequently misdiagnosed as other benign salivary gland tumours. This article reports a case of a 5- month-old infant girl who presented with a rapidly enlarging left cheek and palatal swelling. Computerized tomography revealed the presence of a large expansile, lytic bony lesion in left hard palate. Histopathological diagnosis of myoepithelial carcinoma was made through a biopsy. Neoadjuvant chemotherapy was delivered prior to surgical resection. Reconstructive surgery was deferred until adulthood when the maxilla and mandible have ceased growing. Strict regular follow-up after surgery was prescribed. Patient was disease free four years post surgery with symmetrical face, minimal left infraorbital depression and inconspicuous scar. Total clearance of tumour remains the main treatment of intraoral myoepithelial carcinoma. A good outcome was achieved through a team approach.